Discrepant activity levels of von Willebrand factor-cleaving protease (ADAMTS-13) in congenital thrombotic thrombocytopenic purpura

Blood. 2003 Aug 1;102(3):1148. doi: 10.1182/blood-2003-05-1466.
No abstract available

Publication types

  • Letter
  • Comment

MeSH terms

  • ADAM Proteins
  • ADAMTS13 Protein
  • Blood Preservation
  • Clinical Enzyme Tests / standards
  • Diagnostic Errors
  • Humans
  • Metalloendopeptidases / blood
  • Metalloendopeptidases / deficiency*
  • Purpura, Thrombotic Thrombocytopenic / congenital
  • Purpura, Thrombotic Thrombocytopenic / diagnosis*

Substances

  • ADAM Proteins
  • Metalloendopeptidases
  • ADAMTS13 Protein
  • ADAMTS13 protein, human