Dominant-negative but not gain-of-function effects of a p53.R270H mutation in mouse epithelium tissue after DNA damage

Cancer Res. 2007 May 15;67(10):4648-56. doi: 10.1158/0008-5472.CAN-06-4681.

Abstract

p53 alterations in human tumors often involve missense mutations that may confer dominant-negative or gain-of-function properties. Dominant-negative effects result in inactivation of wild-type p53 protein in heterozygous mutant cells and as such in a p53 null phenotype. Gain-of-function effects can directly promote tumor development or metastasis through antiapoptotic mechanisms or transcriptional activation of (onco)genes. Here, we show, using conditional mouse technology, that epithelium-specific heterozygous expression of mutant p53 (i.e., the p53.R270H mutation that is equivalent to the human hotspot R273H) results in an increased incidence of spontaneous and UVB-induced skin tumors. Expression of p53.R270H exerted dominant-negative effects on latency, multiplicity, and progression status of UVB-induced but not spontaneous tumors. Surprisingly, gain-of-function properties of p53.R270H were not detected in skin epithelium. Apparently, dominant-negative and gain-of-function effects of mutant p53 are highly tissue specific and become most manifest upon stabilization of p53 after DNA damage.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cloning, Molecular
  • DNA Damage / physiology*
  • Epithelium / physiology
  • Epithelium / radiation effects
  • Female
  • Gene Deletion
  • Genes, p53 / genetics*
  • Humans
  • Male
  • Mice
  • Mice, Knockout
  • Mutation*
  • Mutation, Missense
  • Neoplasms, Radiation-Induced / genetics*
  • Skin / metabolism
  • Skin / radiation effects
  • Skin Neoplasms / etiology
  • Skin Neoplasms / genetics*
  • Sunburn / etiology
  • Sunburn / genetics
  • Sunburn / pathology
  • Ultraviolet Rays