Acquired thrombotic thrombocytopenic purpura: ADAMTS13 activity, anti-ADAMTS13 autoantibodies and risk of recurrent disease

Haematologica. 2008 Feb;93(2):172-7. doi: 10.3324/haematol.12701.
No abstract available

Publication types

  • Editorial

MeSH terms

  • ADAM Proteins / genetics
  • ADAM Proteins / immunology*
  • ADAMTS13 Protein
  • Autoantibodies / immunology*
  • Epitopes / genetics
  • Epitopes / immunology*
  • Female
  • Genetic Diseases, Inborn / enzymology
  • Genetic Diseases, Inborn / genetics
  • Genetic Diseases, Inborn / immunology
  • Genetic Diseases, Inborn / mortality
  • Genetic Diseases, Inborn / therapy
  • Genetic Predisposition to Disease / genetics
  • Humans
  • Male
  • Protein Structure, Tertiary / genetics
  • Purpura, Thrombotic Thrombocytopenic / enzymology
  • Purpura, Thrombotic Thrombocytopenic / genetics
  • Purpura, Thrombotic Thrombocytopenic / immunology*
  • Purpura, Thrombotic Thrombocytopenic / mortality
  • Purpura, Thrombotic Thrombocytopenic / therapy
  • Recurrence
  • Risk Factors
  • von Willebrand Factor / genetics
  • von Willebrand Factor / immunology

Substances

  • Autoantibodies
  • Epitopes
  • von Willebrand Factor
  • ADAM Proteins
  • ADAMTS13 Protein
  • ADAMTS13 protein, human