Objective: To report a case in which uterine torsion in a nulligravid female adolescent was noted upon surgical management of complete cervical and partial vaginal agenesis.
Design: Case report.
Setting: University hospital.
Patient(s): A 13-year-old nulligravid adolescent female.
Intervention(s): Ultrasound-guided vaginal exploration, diagnostic laparoscopy, and hysterectomy.
Main outcome measure(s): Uterine torsion as complication of cervical agenesis and its management.
Result(s): Complete cervical agenesis, hematometra, and resultant 180-degree horizontal uterine torsion and sacral entrapment.
Conclusion(s): Cervical agenesis can be a risk factor for uterine torsion. Hysterectomy is a common treatment due to resultant hematometra, pelvic pain, and severe endometriosis, although rare case reports show success with uterovaginal recanalization in cases with cervical dysgenesis.