Metabolism of lysine in alpha-aminoadipic semialdehyde dehydrogenase-deficient fibroblasts: evidence for an alternative pathway of pipecolic acid formation

FEBS Lett. 2010 Jan 4;584(1):181-6. doi: 10.1016/j.febslet.2009.11.055.

Abstract

The mammalian degradation of lysine is believed to proceed via two distinct routes, the saccharopine and the pipecolic acid routes, that ultimately converge at the level of alpha-aminoadipic semialdehyde (alpha-AASA). alpha-AASA dehydrogenase-deficient fibroblasts were grown in cell culture medium supplemented with either L-[alpha-(15)N]lysine or L-[epsilon-(15)N]lysine to explore the exact route of lysine degradation. L-[alpha-(15)N]lysine was catabolised into [(15)N]saccharopine, [(15)N]alpha-AASA, [(15)N]Delta(1)-piperideine-6-carboxylate, and surprisingly in [(15)N]pipecolic acid, whereas L-[epsilon-(15)N]lysine resulted only in the formation of [(15)N]saccharopine. These results imply that lysine is exclusively degraded in fibroblasts via the saccharopine branch, and pipecolic acid originates from an alternative precursor. We hypothesize that pipecolic acid derives from Delta(1)-piperideine-6-carboxylate by the action of Delta(1)-pyrroline-5-carboxylic acid reductase, an enzyme involved in proline metabolism.

MeSH terms

  • Aldehyde Dehydrogenase / deficiency*
  • Cell Line
  • Fibroblasts / enzymology*
  • Humans
  • L-Aminoadipate-Semialdehyde Dehydrogenase
  • Lysine / metabolism*
  • Neoplasm Proteins / deficiency*
  • Picolinic Acids / metabolism
  • Pipecolic Acids / metabolism*
  • Pyrroles / metabolism

Substances

  • Neoplasm Proteins
  • Picolinic Acids
  • Pipecolic Acids
  • Pyrroles
  • delta-1-pyrroline-5-carboxylate
  • delta-1-piperidine-6-carboxylic acid
  • Aldehyde Dehydrogenase
  • AASDH protein, human
  • L-Aminoadipate-Semialdehyde Dehydrogenase
  • pipecolic acid
  • Lysine