Purpose: To describe a rare case of primary conjunctival clear cell carcinoma.
Methods: The clinical history and pathologic findings were reviewed.
Results: An 82-year-old white man presented with a lesion on his right conjunctiva for 8 months. An excisional biopsy was performed with wide margins and mitomycin C. Pathologic examination showed a papillary clear cell carcinoma of the conjunctiva. The patient has been followed for 6 months without recurrence.
Conclusions: Primary clear cell carcinoma, a variant of squamous cell carcinoma, can occur in the conjunctiva.