Electrical storm in short-QT syndrome successfully treated with Isoproterenol

J Cardiovasc Electrophysiol. 2012 Sep;23(9):1028-30. doi: 10.1111/j.1540-8167.2012.02295.x. Epub 2012 Apr 11.

Abstract

Short-QT Syndrome. A 28-year-old man was admitted after aborted sudden cardiac death while sleeping. QTc was 320 ms, suggesting short-QT syndrome (SQTS). The patient then presented with electrical storm with 8 successive episodes of ventricular fibrillation while on deep sedation and hypothermia. Isoproterenol infusion was introduced, leading to rapid cessation of any arrhythmic event. Isoproterenol can be effective in managing electrical storm in patients with SQTS. (J Cardiovasc Electrophysiol, Vol. 23, pp. 1028-1030, September 2012).

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Arrhythmias, Cardiac / drug therapy
  • Arrhythmias, Cardiac / physiopathology*
  • Electrocardiography
  • Heart Conduction System / abnormalities
  • Heart Conduction System / physiopathology
  • Heart Defects, Congenital / drug therapy
  • Heart Defects, Congenital / physiopathology*
  • Humans
  • Isoproterenol / therapeutic use*
  • Male

Substances

  • Isoproterenol

Supplementary concepts

  • Short QT Syndrome 1