Molecular basis of 9G4 B cell autoreactivity in human systemic lupus erythematosus

J Immunol. 2013 Nov 15;191(10):4926-39. doi: 10.4049/jimmunol.1202263. Epub 2013 Oct 9.

Abstract

9G4(+) IgG Abs expand in systemic lupus erythematosus (SLE) in a disease-specific fashion and react with different lupus Ags including B cell Ags and apoptotic cells. Their shared use of VH4-34 represents a unique system to understand the molecular basis of lupus autoreactivity. In this study, a large panel of recombinant 9G4(+) mAbs from single naive and memory cells was generated and tested against B cells, apoptotic cells, and other Ags. Mutagenesis eliminated the framework-1 hydrophobic patch (HP) responsible for the 9G4 idiotype. The expression of the HP in unselected VH4-34 cells was assessed by deep sequencing. We found that 9G4 Abs recognize several Ags following two distinct structural patterns. B cell binding is dependent on the HP, whereas anti-nuclear Abs, apoptotic cells, and dsDNA binding are HP independent and correlate with positively charged H chain third CDR. The majority of mutated VH4-34 memory cells retain the HP, thereby suggesting selection by Ags that require this germline structure. Our findings show that the germline-encoded HP is compulsory for the anti-B cell reactivity largely associated with 9G4 Abs in SLE but is not required for reactivity against apoptotic cells, dsDNA, chromatin, anti-nuclear Abs, or cardiolipin. Given that the lupus memory compartment contains a majority of HP(+) VH4-34 cells but decreased B cell reactivity, additional HP-dependent Ags must participate in the selection of this compartment. This study represents the first analysis, to our knowledge, of VH-restricted autoreactive B cells specifically expanded in SLE and provides the foundation to understand the antigenic forces at play in this disease.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Antibodies, Antinuclear / immunology
  • Apoptosis / immunology
  • Autoantigens / immunology
  • B-Lymphocytes / immunology*
  • Cardiolipins / immunology
  • Chromatin / immunology
  • DNA / immunology
  • Humans
  • Immunoglobulin G / immunology*
  • Immunoglobulin Idiotypes / immunology
  • Immunoglobulin Variable Region / genetics
  • Immunoglobulin Variable Region / immunology*
  • Lupus Erythematosus, Systemic / immunology*
  • Molecular Sequence Data

Substances

  • Antibodies, Antinuclear
  • Autoantigens
  • Cardiolipins
  • Chromatin
  • Immunoglobulin G
  • Immunoglobulin Idiotypes
  • Immunoglobulin Variable Region
  • DNA

Associated data

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