Abstract
Uhl's anomaly is an evolutive disease leading to terminal right ventricular failure. The most difficult differential diagnosis at presentation is the Ebstein disease. We describe the evolution of a foetus with Uhl's anomaly from 21 to 30 weeks of gestation, with progressive reduction in the right ventricular anterior myocardium suggestive of apoptosis, leading to foetal demise.
Keywords:
foetal echocardiography.
MeSH terms
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Cardiomyopathy, Dilated / diagnostic imaging*
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Cardiomyopathy, Dilated / mortality
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Cardiomyopathy, Dilated / pathology
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Diagnosis, Differential
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Female
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Fetal Death / etiology
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Fetus / abnormalities*
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Gestational Age
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Heart Defects, Congenital / diagnostic imaging*
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Heart Defects, Congenital / mortality
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Heart Defects, Congenital / pathology
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Heart Ventricles / diagnostic imaging
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Heart Ventricles / growth & development
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Heart Ventricles / pathology*
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Humans
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Myocardium / pathology*
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Pregnancy
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Prenatal Diagnosis / methods
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Ultrasonography, Prenatal*
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Young Adult