Phosphaturic mesenchymal tumor of the brain without tumor-induced osteomalacia in an 8-year-old girl: case report

J Neurosurg Pediatr. 2016 May;17(5):573-7. doi: 10.3171/2015.9.PEDS14617. Epub 2016 Jan 1.

Abstract

Phosphaturic mesenchymal tumor (mixed connective tissue variant) (PMT-MCT) are tumors that may cause tumor-induced osteomalacia and rarely appear intracranially. The authors describe the case of an 8-year-old girl who was found to have PMT-MCT with involvement of the cerebellar hemisphere and a small tumor pedicle breaching the dura mater and involving the skull. This was removed surgically in gross-total fashion without further complication. Histologically the tumor was confirmed to be a PMT-MCT. There was no evidence of tumor-induced osteomalacia. At the 42-month follow-up, the patient is doing well, has no abnormalities, and is free of recurrence. PMT-MCTs are rare tumors that may involve the brain parenchyma. A gross-total resection may be effective to cure these lesions.

Keywords: ABC = aneurysmal bone cyst; PMT-MCT = phosphaturic mesenchymal tumor (mixed connective tissue variant); RT-PCR = reverse transcriptase polymerase chain reaction; TIO = tumor-induced osteomalacia; cerebellar tumor; fibroblast growth factor 23; oncology; pediatric brain tumor; phosphaturic mesenchymal tumor.

Publication types

  • Case Reports

MeSH terms

  • Ataxia / etiology*
  • Biomarkers, Tumor / analysis*
  • Biomarkers, Tumor / genetics
  • Cerebellar Neoplasms / chemistry
  • Cerebellar Neoplasms / complications
  • Cerebellar Neoplasms / pathology
  • Cerebellar Neoplasms / surgery*
  • Child
  • Diagnosis, Differential
  • Female
  • Fibroblast Growth Factor-23
  • Fibroblast Growth Factors / analysis*
  • Fibroblast Growth Factors / genetics
  • Gene Expression Regulation, Neoplastic
  • Humans
  • Hypophosphatemia / etiology
  • Hypophosphatemia, Familial / etiology*
  • Magnetic Resonance Imaging
  • Mesenchymoma / chemistry
  • Mesenchymoma / complications
  • Mesenchymoma / pathology
  • Mesenchymoma / surgery*
  • Osteomalacia / etiology
  • Reverse Transcriptase Polymerase Chain Reaction
  • Skull Neoplasms / chemistry
  • Skull Neoplasms / complications
  • Skull Neoplasms / pathology
  • Skull Neoplasms / surgery*
  • Tomography, X-Ray Computed
  • Treatment Outcome

Substances

  • Biomarkers, Tumor
  • Fibroblast Growth Factors
  • Fibroblast Growth Factor-23