Reversible profound sensorineural hearing loss due to propranolol sensitive hemangioma in an infant with PHACE syndrome

John N Bangiyev; Richard Gurgel; Sheryll L Vanderhooft; J Fredrik Grimmer

doi:10.1016/j.ijporl.2017.10.006

Reversible profound sensorineural hearing loss due to propranolol sensitive hemangioma in an infant with PHACE syndrome

Int J Pediatr Otorhinolaryngol. 2017 Dec:103:55-57. doi: 10.1016/j.ijporl.2017.10.006. Epub 2017 Oct 5.

Authors

John N Bangiyev¹, Richard Gurgel², Sheryll L Vanderhooft³, J Fredrik Grimmer²

Affiliations

¹ University of Utah, Division of Otolaryngology, United States. Electronic address: jbangiyev@gmail.com.
² University of Utah, Division of Otolaryngology, United States.
³ University of Utah, Division of Pediatric Dermatology, United States.

PMID: 29224766
DOI: 10.1016/j.ijporl.2017.10.006

Abstract

PHACE syndrome is the association of large or segmental infantile hemangiomas of the face or scalp with abnormalities within the posterior fossa, arteries, cardiovascular system, and eyes. We present a case of reversible profound sensorineural hearing loss due to a cerebellopontine angle infantile hemangioma that was successfully treated with propranolol.

Keywords: Cerebello-pontine angle; Hemangioma; Infantile hemangioma; PHACE syndrome; Propranolol; Sensorineural hearing loss; Vascular malformation.

Publication types

Case Reports

MeSH terms

Adrenergic beta-Antagonists / therapeutic use*
Aortic Coarctation / complications*
Eye Abnormalities / complications*
Hearing Loss, Sensorineural / etiology*
Hemangioma / complications*
Hemangioma / drug therapy
Humans
Infant
Magnetic Resonance Imaging
Male
Neurocutaneous Syndromes / complications*
Propranolol / therapeutic use*

Substances

Adrenergic beta-Antagonists
Propranolol

Supplementary concepts

PHACE association