Administration of immunoglobulin G-degrading enzyme of Streptococcus pyogenes (IdeS) for persistent anti-ADAMTS13 antibodies in patients with thrombotic thrombocytopenic purpura in clinical remission

Br J Haematol. 2019 Jul;186(1):137-140. doi: 10.1111/bjh.15706. Epub 2018 Nov 29.
No abstract available

Keywords: TTP; autoimmune disease; clinical trials; thrombotic haemolytic anaemias.

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • ADAMTS13 Protein / immunology*
  • Autoantibodies / immunology*
  • Female
  • Humans
  • Immunoglobulin G / metabolism*
  • Male
  • Purpura, Thrombotic Thrombocytopenic / drug therapy*
  • Purpura, Thrombotic Thrombocytopenic / immunology
  • Remission Induction
  • Streptococcus pyogenes / enzymology

Substances

  • Autoantibodies
  • Immunoglobulin G
  • ADAMTS13 Protein
  • ADAMTS13 protein, human

Associated data

  • ClinicalTrials.gov/NCT02854059