Stealth thrombosis of brain and kidney in a girl with Upshaw-Schulman syndrome not receiving prophylactic plasma infusions

Int J Hematol. 2020 Nov;112(5):603-604. doi: 10.1007/s12185-020-02997-5. Epub 2020 Sep 23.

Saori Tanabe¹, Yoshihiro Fujimura², Bernhard Lämmle^{3

4

5}, Toshiyuki Kimura¹, Ayami Isonishi⁶, Kazuya Sakai⁶, Masanori Matsumoto⁷

¹ Department of Pediatrics, Nihonkai General Hospital, Sakata, Japan.
² Japanese Red Cross Kinki Block Blood Center, Osaka, Japan.
³ Department of Hematology and Central Hematology Laboratory, Inselspital, Bern University Hospital, University of Bern, Bern, Switzerland.
⁴ Center for Thrombosis and Hemostasis, University Medical Center, Mainz, Germany.
⁵ Haemostasis Research Unit, University College London, London, UK.
⁶ Department of Blood Transfusion Medicine, Nara Medical University, Kashihara, Japan.
⁷ Department of Blood Transfusion Medicine, Nara Medical University, Kashihara, Japan. mmatsumo@naramed-u.ac.jp.

No abstract available

Keywords: ADAMTS13 replenishment; Silent cerebral thrombosis; Upshaw–Schulman syndrome.

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