Vestibular Schwannoma

Excerpt

Schwannomas (also known as neuromas, neurinomas "of Verocay," and neurilemmomas) are benign, well-encapsulated, slow-growing nerve sheath tumors composed exclusively of Schwann cells derived from the neural crest. The tumor can originate from any myelinated central or peripheral nerve with Schwann cells. The World Health Organization classifies schwannoma as a grade I benign tumor. Schwannomas are solitary in 90% of the cases. Multiple tumors in the same patient should bring attention to syndromic associations (neurofibromatosis type 2, schwannomatosis, and Carney complex).