This paper presents a summary of information regarding divergence excess exotropia. The first portion of the paper deals with the description (i.e., definition, onset, natural history, prevalence, sexual distribution, symptomatology, and the differential diagnosis of the two subtypes) of this entity. The second portion of the paper reviews the various treatment options (surgery, lens therapy, prism therapy, and vision training) currently available with emphasis on vision training/orthoptics. We conclude that divergence excess exotropia is effectively managed at least as well by vision training/orthoptics as it is by surgery. We propose that future research examine in greater detail the characteristics of the subtypes of this entity to potentially derive improved training techniques for this population.