Retrograde Type A Aortic Dissection 48 Hours after TEVAR in a Patient with a Delayed Diagnosis of Vascular Ehlers-Danlos Syndrome

Ian Diebels; Jeroen M H Hendriks; Joke Durnez; Bernard P Paelinck; Haroun El Addouli; Steven Laga; Bart L Loeys

doi:10.1055/s-0042-1749171

Retrograde Type A Aortic Dissection 48 Hours after TEVAR in a Patient with a Delayed Diagnosis of Vascular Ehlers-Danlos Syndrome

Aorta (Stamford). 2022 Jun;10(3):141-144. doi: 10.1055/s-0042-1749171. Epub 2022 Nov 1.

Authors

Ian Diebels¹, Jeroen M H Hendriks^{1

2}, Joke Durnez^{1

2}, Bernard P Paelinck^{2

3}, Haroun El Addouli^{2

4}, Steven Laga^{2

5}, Bart L Loeys^{2

6}

Affiliations

¹ Department of Thoracic and Vascular Surgery, Antwerp University Hospital, Edegem, Belgium.
² European Reference Network Qualified Aorta Clinic of the Antwerp University Hospital, Antwerp University Hospital, Edegem, Belgium.
³ Department of Cardiology, Antwerp University Hospital, Edegem, Belgium.
⁴ Department of Radiology, Antwerp University Hospital, Edegem, Belgium.
⁵ Department of Cardiac Surgery, Antwerp University Hospital, Edegem, Belgium.
⁶ Department of Genetic Medicine, Antwerp University Hospital, Edegem, Belgium.

Abstract

We report a case of a fatal retrograde Type A aortic dissection following thoracic endovascular aortic repair (TEVAR). The patient was diagnosed with vascular Ehlers-Danlos syndrome (vEDS) only postoperatively, which is a relative contraindication for TEVAR. The patient had no major or minor criteria for vEDS. This case report emphasizes pitfalls of TEVAR in patients with a connective tissue disorder.

The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/).

Grants and funding

Funding None.