An Oncoplastic Approach to Primary Pediatric Pterygomaxillary Osteosarcoma

Cleft Palate Craniofac J. 2023 Mar 27:10556656231154814. doi: 10.1177/10556656231154814. Online ahead of print.

Abstract

Osteosarcomas arising within the pterygomaxillary/infratemporal fossa region are rare among the pediatric population. Survival rates are most influenced by tumor resection with negative margins, which can be dependent on surgical accessibility of the tumor site. The pterygomaxillary/infratemporal fossa location poses several challenges to safe and adequate tumor resection, including proximity of the facial nerve and great vessels and scarring associated with traditional transfacial approaches. In this article, we present the case of a 6-year-old boy with an osteosarcoma of the left pterygomaxillary/infratemporal fossa region successfully managed with an "oncoplastic" approach, incorporating the use of CAD/CAM and mixed reality technologies.

Keywords: CAD/CAM; infratemporal fossa tumor; mixed reality; oncoplastic surgery; pediatric osteosarcoma; pterygomaxillary tumor; virtual planning; virtual reality.