Hepatic perivascular epithelioid cell tumors: The importance of preoperative diagnosis

Shuai Yan; Jia-Jie Lu; Lin Chen; Wei-Hua Cai; Jin-Zhu Wu

doi:10.3748/wjg.v30.i13.1926

Hepatic perivascular epithelioid cell tumors: The importance of preoperative diagnosis

World J Gastroenterol. 2024 Apr 7;30(13):1926-1933. doi: 10.3748/wjg.v30.i13.1926.

Authors

Shuai Yan^{1

2}, Jia-Jie Lu^{1

2}, Lin Chen³, Wei-Hua Cai^{1

2}, Jin-Zhu Wu^{1

4}

Affiliations

¹ Department of Medical School, Nantong University, Nantong 226300, Jiangsu Province, China.
² Department of Hepatobiliary Surgery, Affiliated Nantong Hospital 3 of Nantong University, Nantong 226006, Jiangsu Province, China.
³ Nantong Institute of Liver Disease, Affiliated Nantong Hospital 3 of Nantong University, Nantong 226006, Jiangsu Province, China.
⁴ Department of Hepatobiliary Surgery, Affiliated Nantong Hospital 3 of Nantong University, Nantong 226006, Jiangsu Province, China. wjz1258@163.com.

Abstract

Accurate preoperative diagnosis is highly important for the treatment of perivascular epithelioid cell tumors (PEComas) because PEComas are mainly benign tumors and may not require surgical intervention. By analyzing the causes, properties and clinical manifestations of PEComas, we summarize the challenges and solutions in the diagnosis of PEComas.

Keywords: Angiomyolipomas; Hepatic perivascular epithelioid cell tumors; Liver; Mesenchymal tissue-derived tumors; Preoperative diagnosis.

Publication types

Review

MeSH terms

Biomarkers, Tumor / analysis
Diagnosis, Differential
Hepatectomy
Humans
Liver / diagnostic imaging
Liver / pathology
Liver / surgery
Liver Neoplasms* / diagnosis
Liver Neoplasms* / pathology
Liver Neoplasms* / surgery
Perivascular Epithelioid Cell Neoplasms* / diagnosis
Perivascular Epithelioid Cell Neoplasms* / pathology
Perivascular Epithelioid Cell Neoplasms* / surgery
Preoperative Care / methods

Substances

Biomarkers, Tumor