Effects of fresh plasma or whole blood transfusions on patients with various types of mucopolysaccharidosis

Pediatrics. 1972 Nov;50(5):688-92.
No abstract available

MeSH terms

  • Adolescent
  • Adrenal Cortex Hormones / therapeutic use
  • Blood Transfusion*
  • Carbohydrate Metabolism, Inborn Errors / drug therapy
  • Carbohydrate Metabolism, Inborn Errors / therapy
  • Cetylpyridinium / urine
  • Child
  • Child, Preschool
  • Chromatography, Gel
  • Creatine / urine
  • Female
  • Glycosaminoglycans / analysis
  • Glycosaminoglycans / cerebrospinal fluid
  • Glycosaminoglycans / metabolism*
  • Glycosaminoglycans / urine
  • Humans
  • Intellectual Disability / therapy
  • Intelligence Tests
  • Male
  • Molecular Weight
  • Mucopolysaccharidoses / therapy
  • Plasma*
  • Retinitis Pigmentosa / therapy

Substances

  • Adrenal Cortex Hormones
  • Glycosaminoglycans
  • Cetylpyridinium
  • Creatine