Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism

J Inherit Metab Dis. 1994;17(5):611-5. doi: 10.1007/BF00711600.

Authors

N Sugiyama¹, I Matsuda, Y Wada, K Narisawa, M Kobayashi, K Kidouchi

Affiliation

¹ Department of Pediatrics, Nagoya City University Medical School, Japan.

PMID: 7837769
DOI: 10.1007/BF00711600

No abstract available

MeSH terms

Adolescent
Carnitine / administration & dosage
Carnitine / analogs & derivatives*
Carnitine / therapeutic use*
Carnitine / urine
Child
Child, Preschool
Female
Humans
Infant
Male
Metabolism, Inborn Errors / drug therapy*
Metabolism, Inborn Errors / urine
Propionates / metabolism*

Substances

Propionates
propionylcarnitine
propionic acid
Carnitine