Costameric distribution of beta-dystroglycan (43 kDa dystrophin-associated glycoprotein) in normal and dystrophin-deficient human skeletal muscle

Biochem Soc Trans. 1996 May;24(2):501-6. doi: 10.1042/bst0240501.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Actinin / analysis
  • Biopsy
  • Blotting, Western
  • Cytoskeletal Proteins / analysis
  • Cytoskeletal Proteins / deficiency
  • Cytoskeletal Proteins / metabolism*
  • Dystroglycans
  • Dystrophin / metabolism
  • Humans
  • Immunohistochemistry
  • Membrane Glycoproteins / analysis
  • Membrane Glycoproteins / deficiency
  • Membrane Glycoproteins / metabolism*
  • Muscle Fibers, Skeletal / metabolism
  • Muscle Fibers, Skeletal / pathology
  • Muscle, Skeletal / cytology
  • Muscle, Skeletal / metabolism*
  • Muscle, Skeletal / pathology
  • Muscular Dystrophies / genetics
  • Muscular Dystrophies / metabolism
  • Muscular Dystrophies / pathology

Substances

  • Cytoskeletal Proteins
  • DAG1 protein, human
  • Dystrophin
  • Membrane Glycoproteins
  • Actinin
  • Dystroglycans