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Muscle LIM Protein Force-Sensing Mediates Sarcomeric Biomechanical Signaling in Human Familial Hypertrophic Cardiomyopathy.
Circulation. 2022 Apr 19;145(16):1238-1253. doi: 10.1161/CIRCULATIONAHA.121.056265. Epub 2022 Apr 6.
Circulation. 2022.
PMID: 35384713
Free PMC article.
Familial dilated cardiomyopathy diagnosis is commonly overlooked at the time of transplant listing.
Seidelmann SB, Laur O, Hwa J, Depasquale E, Bellumkonda L, Sugeng L, Pomianowski P, Testani J, Chen M, McKenna W, Jacoby D.
Seidelmann SB, et al.
J Heart Lung Transplant. 2016 Apr;35(4):474-80. doi: 10.1016/j.healun.2015.12.002. Epub 2015 Dec 11.
J Heart Lung Transplant. 2016.
PMID: 26852066
Free PMC article.
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Practical genetics of thoracic aortic aneurysm.
Elefteriades JA, Pomianowski P.
Elefteriades JA, et al.
Prog Cardiovasc Dis. 2013 Jul-Aug;56(1):57-67. doi: 10.1016/j.pcad.2013.06.002.
Prog Cardiovasc Dis. 2013.
PMID: 23993238
Review.
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The genetics and genomics of thoracic aortic disease.
Pomianowski P, Elefteriades JA.
Pomianowski P, et al.
Ann Cardiothorac Surg. 2013 May;2(3):271-9. doi: 10.3978/j.issn.2225-319X.2013.05.12.
Ann Cardiothorac Surg. 2013.
PMID: 23977594
Free PMC article.
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Genomic characterization of prenatally detected chromosomal structural abnormalities using oligonucleotide array comparative genomic hybridization.
Li P, Pomianowski P, DiMaio MS, Florio JR, Rossi MR, Xiang B, Xu F, Yang H, Geng Q, Xie J, Mahoney MJ.
Li P, et al.
Am J Med Genet A. 2011 Jul;155A(7):1605-15. doi: 10.1002/ajmg.a.34043. Epub 2011 Jun 10.
Am J Med Genet A. 2011.
PMID: 21671377
Free PMC article.
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Ceramide recruits and activates protein kinase C zeta (PKC zeta) within structured membrane microdomains.
Fox TE, Houck KL, O'Neill SM, Nagarajan M, Stover TC, Pomianowski PT, Unal O, Yun JK, Naides SJ, Kester M.
Fox TE, et al. Among authors: pomianowski pt.
J Biol Chem. 2007 Apr 27;282(17):12450-7. doi: 10.1074/jbc.M700082200. Epub 2007 Feb 17.
J Biol Chem. 2007.
PMID: 17308302
Free article.
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