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Page 1
Hypersensitivity pneumonitis in a cystic fibrosis patient.
Occup Med (Lond). 2019 Dec 31;69(8-9):632-634. doi: 10.1093/occmed/kqz115.
Occup Med (Lond). 2019.
PMID: 31504833
Rapid Improvement after Starting Elexacaftor-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and Advanced Pulmonary Disease.
Burgel PR, Durieu I, Chiron R, Ramel S, Danner-Boucher I, Prevotat A, Grenet D, Marguet C, Reynaud-Gaubert M, Macey J, Mely L, Fanton A, Quetant S, Lemonnier L, Paillasseur JL, Da Silva J, Martin C; French Cystic Fibrosis Reference Network Study Group.
Burgel PR, et al.
Am J Respir Crit Care Med. 2021 Jul 1;204(1):64-73. doi: 10.1164/rccm.202011-4153OC.
Am J Respir Crit Care Med. 2021.
PMID: 33600738
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AGER -429T/C is associated with an increased lung disease severity in cystic fibrosis.
Beucher J, Boëlle PY, Busson PF, Muselet-Charlier C, Clement A, Corvol H; French C F Modifier Gene Study Investigators.
Beucher J, et al.
PLoS One. 2012;7(7):e41913. doi: 10.1371/journal.pone.0041913. Epub 2012 Jul 30.
PLoS One. 2012.
PMID: 22860029
Free PMC article.
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Reference percentiles for FEV(1) and BMI in European children and adults with cystic fibrosis.
Boëlle PY, Viviani L, Busson PF, Olesen HV, Ravilly S, Stern M, Assael BM, Barreto C, Drevinek P, Thomas M, Krivec U, Mei-Zahav M, Vibert JF, Clement A, Mehta A, Corvol H; French CF Modifier Gene Study Investigators; European CF Registry Working Group.
Boëlle PY, et al.
Orphanet J Rare Dis. 2012 Sep 7;7:64. doi: 10.1186/1750-1172-7-64.
Orphanet J Rare Dis. 2012.
PMID: 22958330
Free PMC article.
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Cephalic versus oronasal mask for noninvasive ventilation in acute hypercapnic respiratory failure.
Cuvelier A, Pujol W, Pramil S, Molano LC, Viacroze C, Muir JF.
Cuvelier A, et al. Among authors: pramil s.
Intensive Care Med. 2009 Mar;35(3):519-26. doi: 10.1007/s00134-008-1327-x. Epub 2008 Oct 15.
Intensive Care Med. 2009.
PMID: 18854973
Clinical Trial.
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High frequency of voriconazole-related phototoxicity in cystic fibrosis patients.
Rondeau S, Couderc L, Dominique S, Pramil S, Leguillon C, Masseline B, Favennec L, Marguet C.
Rondeau S, et al. Among authors: pramil s.
Eur Respir J. 2012 Mar;39(3):782-4. doi: 10.1183/09031936.00097611.
Eur Respir J. 2012.
PMID: 22379155
Free article.
No abstract available.
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