Orbital lymphangioma: an analysis of 26 patients

Br J Ophthalmol. 1999 Jan;83(1):76-80. doi: 10.1136/bjo.83.1.76.

Abstract

Aim: To evaluate retrospective data on the clinical findings, histological features, radiological diagnosis, and management outcomes in orbital lymphangioma.

Methods: Data on 26 orbital lymphangioma patients managed over 16 years were re-evaluated. The computed tomograph and magnetic resonance scans and histological slides were reviewed. Parametric techniques were used to assess correlations among clinical, radiological, and histopathological factors.

Results: At presentation proptosis was present in 85%, ptosis in 73%, and restrictive eye movements in 46% of patients. The accuracy of the initial radiology interpretations was 77%. 24 cases required one or more surgeries. The mean follow up was 9.2 years (range 1-14 years). 58% of patients developed recurrences. In cases that recurred, motility restriction was significantly more frequent at initial examination than cases without recurrence (p < 0.05). After therapy, 75% of patients were satisfied with their visual function and cosmetic appearance.

Conclusions: Conservative management of orbital lymphangioma with multiple partial resections may achieve satisfactory results.

MeSH terms

  • Adolescent
  • Aged
  • Child
  • Child, Preschool
  • Female
  • Follow-Up Studies
  • Humans
  • Infant
  • Lymphangioma* / diagnostic imaging
  • Lymphangioma* / pathology
  • Lymphangioma* / surgery
  • Magnetic Resonance Imaging / methods
  • Male
  • Middle Aged
  • Neoplasm Recurrence, Local
  • Orbital Neoplasms* / diagnostic imaging
  • Orbital Neoplasms* / pathology
  • Orbital Neoplasms* / surgery
  • Retrospective Studies
  • Sensitivity and Specificity
  • Tomography, X-Ray Computed / methods
  • Treatment Outcome
  • Visual Acuity