Docosahexaenoic acid and retinal function in children with long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency

J Inherit Metab Dis. 1999 May;22(3):276-80. doi: 10.1023/a:1005502626406.
No abstract available

Publication types

  • Clinical Trial
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • 3-Hydroxyacyl CoA Dehydrogenases / deficiency*
  • Adolescent
  • Child
  • Child, Preschool
  • Dietary Fats / metabolism*
  • Docosahexaenoic Acids / metabolism*
  • Humans
  • Infant
  • Lipid Metabolism, Inborn Errors / complications
  • Lipid Metabolism, Inborn Errors / drug therapy
  • Lipid Metabolism, Inborn Errors / physiopathology
  • Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase
  • Retina / physiopathology*
  • Retinitis Pigmentosa / etiology*
  • Retinitis Pigmentosa / physiopathology

Substances

  • Dietary Fats
  • Docosahexaenoic Acids
  • 3-Hydroxyacyl CoA Dehydrogenases
  • Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase