Case report: We report a rare case of a unique variant of schwannoma (neuroblastoma-like schwannoma) in the orbit in a 16-year-old male who presented with proptosis and decreased vision.
Comment: Schwannoma with giant rosettes and hyperchromatic small cells was previously designated a neuroblastoma-like schwannoma by Goldblum et al. (Am J Surg Pathol 1994;18[3]:266-73). In the past, 9 cases of this variant of schwannoma have been reported as a painless subcutaneous nodule in various parts of the body, but none has been reported in the orbit so far. This entity must be distinguished from neuroblastoma, neuroectodermal tumor, and malignant change in schwannoma.