A solitary mediastinal mass due to localized AL amyloidosis: case report and review of the literature

Amyloid. 2013 Jun;20(2):127-30. doi: 10.3109/13506129.2013.775644. Epub 2013 Mar 6.

Abstract

AL amyloidosis presenting as a solitary mediastinal mass is a rare occurrence, with only a few cases reported in the literature. We describe a case of a man presenting with a mediastinal mass diagnosed as amyloidosis, confirmed by mass spectrometry to consist of lambda light chains. Here we review the literature and discuss treatment options for this rare entity.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aged
  • Amyloid / metabolism*
  • Amyloidosis / complications*
  • Amyloidosis / diagnosis
  • Amyloidosis / metabolism
  • Humans
  • Immunoglobulin lambda-Chains / metabolism*
  • Male
  • Mediastinal Diseases / diagnosis
  • Mediastinal Diseases / etiology*
  • Mediastinal Diseases / metabolism
  • Review Literature as Topic
  • Spectrometry, Mass, Matrix-Assisted Laser Desorption-Ionization
  • Tomography, X-Ray Computed

Substances

  • Amyloid
  • Immunoglobulin lambda-Chains
  • amyloid L, human