Retinal detachments involving the posterior pole in hallermann-streiff syndrome

Retin Cases Brief Rep. 2011 Winter;5(1):70-2. doi: 10.1097/ICB.0b013e3181babe38.

Abstract

Purpose: To report a case of Hallermann-Streiff syndrome and bilateral retinal detachments involving the posterior pole.

Methods: Retrospective case report and literature review.

Results: A 2-year-old girl with Hallermann-Streiff syndrome was evaluated. Fundus examination showed bilateral exudative retinal detachments involving a significant portion of the posterior pole. The left eye showed several large, cyst-like areas of retinal detachment. The child was observed without treatment, and the subretinal fluid remained stable during the follow-up of 10 months.

Conclusion: Bilateral retinal detachments can be seen in patients with Hallermann-Streiff syndrome. The etiology is likely to be multifactorial, and uveal effusion may contribute to the exudative fluid. Further evaluation is necessary to determine the visual prognosis and optimal management of patients with exudative retinal detachments associated with Hallermann-Streiff syndrome.