Purpose: To report the association of an orbital osteoma with Gardner's syndrome (familial polyposis coli leading to carcinoma, multiple osteomas and skin and soft tissue tumours).
Method: A review of patient records.
Results: A 29-year-old male with known Gardner's syndrome presented with long-standing right proptosis due to an osteoma of the medial wall and roof of the orbit. He had previously had prophylactic colectomy and one other osteoma of the skull excised.
Conclusion: Although orbital osteoma in the setting of Gardner's syndrome is rare, it should be recognized as an association because of the importance of the intestinal polyposis, which leads to carcinoma if untreated.