EXTREME HEMOLYSIS AND RED-CELL DISTORTION IN ERYTHROCYTE PYRUVATE KINASE DEFICIENCY. II. MEASUREMENTS OF ERYTHROCYTE GLUCOSE CONSUMPTION, POTASSIUM FLUX AND ADENOSINE TRIPHOSPHATE STABILITY

N Engl J Med. 1965 Jan 21:272:118-23. doi: 10.1056/NEJM196501212720302.
No abstract available

MeSH terms

  • Adenosine Triphosphate*
  • Anemia, Hemolytic*
  • Anemia, Hemolytic, Congenital Nonspherocytic*
  • Biological Transport
  • Child
  • Erythrocytes*
  • Folic Acid*
  • Glucose*
  • Hemolysis*
  • Humans
  • Metabolism, Inborn Errors*
  • Potassium*
  • Pyruvate Kinase*
  • Pyruvate Metabolism, Inborn Errors
  • Reticulocytes*
  • Vitamin B 12*

Substances

  • Adenosine Triphosphate
  • Folic Acid
  • Pyruvate Kinase
  • Glucose
  • Vitamin B 12
  • Potassium

Supplementary concepts

  • Pyruvate Kinase Deficiency of Red Cells