Abstract
A patient presenting with von Hippel-Lindau's disease, syringomyelia, bilateral pheochromocytoma and a multihormonal pancreatic tumor is described. We suggest that this syndrome results from a complex neuroendocrine disorder.
MeSH terms
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Adenoma / pathology
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Adrenal Gland Neoplasms / complications*
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Adrenal Gland Neoplasms / pathology
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Adult
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Angiomatosis / complications*
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Angiomatosis / pathology
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Autopsy
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Humans
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Male
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Pancreatic Neoplasms / complications*
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Pancreatic Neoplasms / pathology
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Pheochromocytoma / complications*
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Pheochromocytoma / pathology
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Retinal Vessels*
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Syndrome
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Syringomyelia / complications*
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Syringomyelia / pathology