Von Hippel-Lindau's Disease, syringomyelia and multiple endocrine tumors: a complex neuroendocrinopathy

Virchows Arch A Pathol Anat Histol. 1978 Jun 15;378(3):265-72. doi: 10.1007/BF00427365.

Abstract

A patient presenting with von Hippel-Lindau's disease, syringomyelia, bilateral pheochromocytoma and a multihormonal pancreatic tumor is described. We suggest that this syndrome results from a complex neuroendocrine disorder.

Publication types

  • Case Reports

MeSH terms

  • Adenoma / pathology
  • Adrenal Gland Neoplasms / complications*
  • Adrenal Gland Neoplasms / pathology
  • Adult
  • Angiomatosis / complications*
  • Angiomatosis / pathology
  • Autopsy
  • Humans
  • Male
  • Pancreatic Neoplasms / complications*
  • Pancreatic Neoplasms / pathology
  • Pheochromocytoma / complications*
  • Pheochromocytoma / pathology
  • Retinal Vessels*
  • Syndrome
  • Syringomyelia / complications*
  • Syringomyelia / pathology