Fatal acute lymphoblastic leukemia in mice transgenic for B cell-restricted bcl-xL and c-myc

J Immunol. 2004 Jun 1;172(11):6684-91. doi: 10.4049/jimmunol.172.11.6684.

Abstract

Expression of the c-myc gene is frequently dysregulated in malignant tumors and translocations of c-myc into the Ig H chain locus are associated with Burkitt's-type lymphoma. There is indirect evidence that bcl-x, an anti-apoptotic member of the bcl-2 gene family, may also contribute to a variety of B lymphoid tumors. In this study, we show that mice transgenic for both B cell-restricted c-myc and bcl-x(L) developed aggressive, acute leukemias expressing early B lineage and stem cell surface markers. Of interest, the tumor cells proliferated and differentiated down the B cell developmental pathway following in vitro treatment with IL-7. Analysis of sorted leukemic cells from spleen indicated constitutive expression of sterile micro and kappa transcripts in combination with evidence for D-J(H) DNA rearrangements. Several B cell-specific genes were either not expressed or were expressed at low levels in primary tumor cells and were induced following culture with IL-7. IL-7 also increased V-Jkappa and V-DJ(H) rearrangements. These data demonstrate oncogenic synergy between c-myc and bcl-x(L) in a new mouse model for acute lymphoblastic leukemia. Tumors in these animals target an early stage in B cell development characterized by the expression of both B lineage and stem cell genes.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Cells, Cultured
  • Gene Rearrangement
  • Genes, Immunoglobulin
  • Genes, myc / physiology*
  • Immunophenotyping
  • Interleukin-7 / pharmacology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / etiology*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / immunology
  • Proto-Oncogene Proteins c-bcl-2 / physiology*
  • bcl-X Protein

Substances

  • Bcl2l1 protein, mouse
  • Interleukin-7
  • Proto-Oncogene Proteins c-bcl-2
  • bcl-X Protein