Stridor is a common presentation to the pediatric emergency department. The differential diagnosis is broad and includes conditions that range from benign to immediately life threatening. The evaluation and management of pediatric patients with stridor can vary, depending on the likely diagnoses and the acuity of the presentation. We report a case of an infant with known myelomeningocele who presented to the emergency department with stridor and the use of ultrasound to diagnose Chiari crisis as the etiology of her symptoms.