Primary intestinal lymphangiectasia as a component of autoimmune polyglandular syndrome type I: a report of 2 cases

Indian J Gastroenterol. 2007 Nov-Dec;26(6):293-5.

Abstract

Chronic diarrhea and steatorrhea occur frequently in patients with autoimmune polyglandular syndrome (APS) type I. Intestinal lymphangiectasia has been reported earlier as a cause of steatorrhea in a young girl with APS Type I. We describe 2 patients with APS Type I who were found to have intestinal lymphangiectasia, one of whom had symptomatic protein-losing enteropathy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Humans
  • Lymphangiectasis, Intestinal / diagnosis
  • Lymphangiectasis, Intestinal / etiology*
  • Male
  • Polyendocrinopathies, Autoimmune / complications*
  • Polyendocrinopathies, Autoimmune / diagnosis