Cardiovascular magnetic resonance diagnosis of a previously unreported association: cor triatriatum with right partial anomalous pulmonary venous return to the azygos vein

Int J Cardiol. 2009 Jul 10;135(3):e80-2. doi: 10.1016/j.ijcard.2008.04.041. Epub 2008 Jul 18.

Abstract

We present images from a cardiovascular magnetic resonance (CMR) study that enabled the rapid, non-invasive, complete diagnosis of a previously unreported congenital anomaly. Cor triatriatum of the left atrium thought to be an anomaly of the embryonic pulmonary venous connection to the left atrium. In association with this, many types of partially anomalous pulmonary venous connection are described, but we know of no previous description of pulmonary venous egress occurring on the right side, via the azygos vein.

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Adult
  • Azygos Vein / abnormalities*
  • Azygos Vein / pathology
  • Cor Triatriatum / diagnosis*
  • Cor Triatriatum / pathology*
  • Cor Triatriatum / therapy
  • Female
  • Heart Atria / abnormalities*
  • Heart Atria / pathology
  • Humans
  • Magnetic Resonance Imaging, Cine / methods
  • Pulmonary Veins / abnormalities*
  • Pulmonary Veins / pathology