Introduction: Leiomyoma is the most common tumor in the uterus. A spectrum of histologic variants have been noted, however, metaplasia in the leiomyoma is a rare phenomenon. Adipose metaplasia being most commonly reported. Cartilaginous metaplasia in leiomyoma is very rare.
Materials and methods: We report first case of pure cartilaginous metaplasia in a uterine leiomyoma.
Conclusion: Cartilaginous areas although rare, may appear in uterine leiomyoma.