Inflammatory epidermolysis bullosa acquisita mimicking toxic epidermal necrolysis and dermatitis herpetiformis

Clin Exp Dermatol. 2009 Dec;34(8):e705-8. doi: 10.1111/j.1365-2230.2009.03439.x. Epub 2009 Jul 29.

Abstract

We report a patient with a spectrum of clinical features simulating toxic epidermal necrolysis, bullous erythema multiforme and later, dermatitis herpetiformis (DH). The histological features were suggestive of DH, bullous pemphigoid (BP) and epidermolysis bullosa acquisita (EBA). Direct immunofluorescence results suggested BP or EBA. Indirect immunofluorescence on salt-split skin and immunoblotting analysis on normal human dermal extracts gave results that were diagnostic for EBA.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Autoantibodies / metabolism
  • Dermatitis Herpetiformis / drug therapy
  • Dermatitis Herpetiformis / pathology*
  • Diagnosis, Differential
  • Epidermolysis Bullosa Acquisita / drug therapy
  • Epidermolysis Bullosa Acquisita / pathology*
  • Fluorescent Antibody Technique, Indirect
  • Humans
  • Immunoglobulin A / metabolism
  • Immunoglobulin G / metabolism
  • Male
  • Stevens-Johnson Syndrome / drug therapy
  • Stevens-Johnson Syndrome / pathology*

Substances

  • Autoantibodies
  • Immunoglobulin A
  • Immunoglobulin G