Early surgical management of chylothorax complicated by Gorham's disease

Thorac Cardiovasc Surg. 2010 Dec;58(8):492-3. doi: 10.1055/s-0030-1250158. Epub 2010 Nov 25.

Abstract

Gorham's disease is a rare disorder and its etiology remains unknown. It is characterized by the proliferation of vascular structures in bone, and results in progressive osteolysis. Chylothorax is a severe complication of Gorham's disease with a mortality of 50%. We report a 14-year-old boy with Gorham's disease complicated by chylothorax who underwent early surgical management followed by radiotherapy.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Biopsy
  • Chylothorax / diagnostic imaging
  • Chylothorax / etiology
  • Chylothorax / surgery*
  • Humans
  • Ligation
  • Male
  • Osteolysis, Essential / complications
  • Osteolysis, Essential / pathology
  • Osteolysis, Essential / radiotherapy
  • Osteolysis, Essential / surgery*
  • Thoracic Duct / surgery*
  • Thoracotomy*
  • Time Factors
  • Tomography, X-Ray Computed
  • Treatment Outcome