Atypical lupus erythematosus panniculitis progressing to antinuclear antibody-negative systemic lupus erythematosus

J Cutan Med Surg. 2012 Sep-Oct;16(5):361-4. doi: 10.1177/120347541201600516.

Abstract

Background: Lupus erythematosus panniculitis (LEp) is an uncommon but distinctive subset of lupus erythematosus (LE). It may develop in patients with discoid or systemic LE or may occur as an isolated phenomenon.

Case report: We describe a case of LEp affecting unusual sites: the parotid gland, eyelid, and scalp. Subsequently, the patient progressed to antinuclear antibody-negative systemic LE.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antibodies, Antinuclear / immunology*
  • Biopsy
  • Diagnosis, Differential
  • Follow-Up Studies
  • Humans
  • Lupus Erythematosus, Systemic / complications*
  • Lupus Erythematosus, Systemic / diagnosis
  • Lupus Erythematosus, Systemic / immunology
  • Male
  • Panniculitis, Lupus Erythematosus / etiology*
  • Panniculitis, Lupus Erythematosus / immunology
  • Panniculitis, Lupus Erythematosus / pathology
  • Skin / pathology*
  • Tomography, X-Ray Computed

Substances

  • Antibodies, Antinuclear