The case of an infant with double outlet right ventricle with anatomically corrected malposition of the great arteries, bilateral infundibulum, and an echocardiographically routable ventricular septal defect (VSD) is presented. After numerous efforts to visualize the margins of the VSD, the best surgical exposure of the VSD was through the aorta. We believe this to be the first report of this phenomenon, which results from the left-sided position of the aorta and the presence of left juxtaposition of the atrial appendages.
Keywords: DORV; anatomically corrected malposition of the great arteries juxtaposition of atrial appendage.