Congenital vascular rings: a clinical challenge for the pediatrician

Pediatr Pulmonol. 2015 May;50(5):511-24. doi: 10.1002/ppul.23152. Epub 2015 Jan 20.

Abstract

Vascular rings are congenital anomalies that lead to variable degrees of respiratory problems or feeding difficulties by forming a complete or partial ring compressing the trachea, the bronchi, and the esophagus. The clinical diagnosis of vascular rings is often challenging for the pediatrician because the clinical manifestations are heterogeneous and nonspecific. Symptoms can vary from wheezing, stridor, dyspnea, and/or dysphagia to life-threatening conditions; however, they may not be present. The aim of this study is to review the recent literature on this subject and describe new developments in diagnostics and imaging.

Keywords: Vascular rings; cardiovascular anomalies; dysphagia; stridor; trachea-esophageal compression.

Publication types

  • Review

MeSH terms

  • Aorta, Thoracic / abnormalities
  • Aorta, Thoracic / embryology
  • Brachiocephalic Trunk / abnormalities
  • Brachiocephalic Trunk / embryology
  • Bronchi
  • Deglutition Disorders / etiology*
  • Dyspnea / etiology*
  • Esophagus
  • Humans
  • Infant
  • Pressure
  • Pulmonary Artery / abnormalities
  • Pulmonary Artery / embryology
  • Respiratory Sounds / etiology*
  • Subclavian Artery / abnormalities
  • Subclavian Artery / embryology
  • Trachea
  • Vascular Malformations / complications*
  • Vascular Malformations / diagnosis
  • Vascular Malformations / embryology