Studies of novel variants associated with Hb F in Sardinians and Tanzanians in sickle cell disease patients from Cameroon

Hemoglobin. 2016 Nov;40(6):377-380. doi: 10.1080/03630269.2016.1251453. Epub 2016 Nov 10.

Abstract

High level of Hb F has been shown to improve survival in sickle cell disease. Among 453 Cameroonians with sickle cell disease, we have investigated 18 selected single-nucleotide polymorphisms (SNPs) in novel and suggestive loci associated with Hb F level identified through a genomewide association study in sickle cell disease patients in Tanzania, and whole-genome sequencing of a population from Sardinia. Seven of 10 variants reported in Sardinians were either monomorphic or very rare in the Cameroonians. No associations were observed with any SNPs and Hb F levels in Cameroonians affected by sickle cell disease. The present study illustrates the complexity of replicating Hb F-promoting variants association results across populations.

Keywords: Cameroon; Hb F; Sardinia; Tanzania; sickle cell disease.

MeSH terms

  • Adolescent
  • Adult
  • Anemia, Sickle Cell / blood
  • Anemia, Sickle Cell / epidemiology
  • Anemia, Sickle Cell / genetics*
  • Cameroon / epidemiology
  • Child
  • Child, Preschool
  • Female
  • Fetal Hemoglobin / analysis*
  • Fetal Hemoglobin / genetics
  • Genetic Variation*
  • Genome-Wide Association Study
  • Humans
  • Italy / epidemiology
  • Male
  • Middle Aged
  • Polymorphism, Single Nucleotide
  • Sequence Analysis, DNA
  • Tanzania / epidemiology
  • Young Adult

Substances

  • Fetal Hemoglobin