A rare variant of intracardiac total anomalous pulmonary venous connection

Rev Port Cardiol. 2017 Nov;36(11):869.e1-869.e4. doi: 10.1016/j.repc.2017.03.009. Epub 2017 Nov 8.
[Article in English, Portuguese]

Abstract

Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber.

Keywords: Cardiac total anomalous pulmonary venous connection; Conexão anómala total das veias pulmonares; Conexão anómala total de veias pulmonares cardíaca; Conexão anómala total de veias pulmonares supracardíaca; Supracardiac total anomalous pulmonary venous connection; Total anomalous pulmonary venous connection.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple* / diagnostic imaging
  • Echocardiography
  • Heart Atria / abnormalities*
  • Heart Atria / diagnostic imaging
  • Humans
  • Infant
  • Male
  • Scimitar Syndrome / classification*
  • Scimitar Syndrome / diagnostic imaging