Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome

Houda Ajmi; Nadia Arifa; Essia Boughzela; Lotfi Ben Mime

doi:10.1093/ejcts/ezy446

Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome

Eur J Cardiothorac Surg. 2019 Aug 1;56(2):409-411. doi: 10.1093/ejcts/ezy446.

Authors

Houda Ajmi¹, Nadia Arifa², Essia Boughzela³, Lotfi Ben Mime⁴

Affiliations

¹ Department of Pediatrics, Sahloul Teaching Hospital, University of Sousse, Sousse, Tunisia.
² Department of Radiology, Sahloul Teaching Hospital, University of Sousse, Sousse, Tunisia.
³ Department of Cardiology, Sahloul Teaching Hospital, University of Sousse, Sousse, Tunisia.
⁴ Department of Pediatric Cardiac Surgery, Pediatric Heart Center Duisburg, University of Duesseldorf, Duesseldorf, Germany.

PMID: 30608517
DOI: 10.1093/ejcts/ezy446

Abstract

In this study, we describe the case of a 5-year-old boy who presumably presented with Loeys-Dietz syndrome. A huge aneurysm of the ascending aorta and the aortic arch extended beyond the left subclavian artery and was accompanied by a slight narrowing of the aortic isthmus.

Keywords: Aortic aneurysm; Aortic valve-sparing surgery; Loeys–Dietz syndrome.

Publication types

Case Reports

MeSH terms

Aorta, Thoracic / surgery*
Aortic Valve / surgery*
Blood Vessel Prosthesis Implantation / methods*
Child, Preschool
Humans
Loeys-Dietz Syndrome / surgery*
Male