Choroid Plexus Papilloma

Excerpt

Choroid plexus papillomas are rare central nervous system tumors, comprising less than 1% of all brain tumors. Although choroid plexus papillomas may occur at any age, 70% of patients with this neoplasm are less than 2 years of age. Choroid plexus papillomas are neuroepithelial tumors that are World Health Organization grade I or II. In contrast, the rarely encountered choroid plexus carcinoma is classified as World Health Organization grade III. Choroid plexus papillomas are more common in the infratentorial compartment in adults and the supratentorial compartment in children. Patients with choroid plexus papillomas often present with communicating hydrocephalus secondary to cerebrospinal fluid overproduction. The prognosis of these benign neoplasms is favorable, and gross total resection is frequently curative.