Heart Failure Following Sinus Venosus Defect Closure in a Patient With Vein of Galen Malformation

David Liddle; Bishoy Ibrahim; Christopher Isibor; Jennifer Judge; Darren B Orbach; Susan F Saleeb

doi:10.1016/j.jaccas.2023.101831

Heart Failure Following Sinus Venosus Defect Closure in a Patient With Vein of Galen Malformation

JACC Case Rep. 2023 Apr 14:14:101831. doi: 10.1016/j.jaccas.2023.101831. eCollection 2023 May 17.

Authors

David Liddle¹, Bishoy Ibrahim², Christopher Isibor³, Jennifer Judge³, Darren B Orbach^{3

4}, Susan F Saleeb^{1

5}

Affiliations

¹ Department of Cardiology, Boston Children's Hospital, Boston, Massachusetts, USA.
² University of Connecticut School of Medicine, Farmington, Connecticut, USA.
³ Department of Neurosurgery, Boston Children's Hospital, Boston, Massachusetts, USA.
⁴ Neurointerventional Radiology, Boston Children's Hospital, Boston, Massachusetts, USA.
⁵ Department of Pediatrics, Harvard Medical School, Boston, Massachusetts, USA.

Abstract

This case concerns an 18-month-old with masked congestive heart failure (CHF) from an unrepaired vein of Galen malformation and superior sinus venosus defect who progressed to severe, refractory CHF following superior sinus venosus defect repair. Partial transvenous coil embolization of a very-high-risk vein of Galen malformation resolved CHF symptoms. (Level of Difficulty: Advanced.).

Keywords: cardiac magnetic resonance; congenital heart defect; echocardiography; imaging; left ventricle.

Publication types

Case Reports