Esophageal Cicatricial Pemphigoid

Sharon Udemba; Ryan Burkholder; Fnu Raja; Michael S Kurin

doi:10.14309/crj.0000000000001149

Esophageal Cicatricial Pemphigoid

ACG Case Rep J. 2024 Jan 25;11(1):e01149. doi: 10.14309/crj.0000000000001149. eCollection 2024 Jan.

Authors

Sharon Udemba¹, Ryan Burkholder², Fnu Raja³, Michael S Kurin²

Affiliations

¹ Department of Medicine, MetroHealth Medical Center, Case Western Reserve University, Cleveland, OH.
² Department of Gastroenterology and Hepatology, MetroHealth Medical Center, Case Western Reserve University, Cleveland, OH.
³ Department of Pathology, MetroHealth Medical Center, Case Western Reserve University, Cleveland, OH.

Abstract

Cicatricial pemphigoid (CP) is a rare autoimmune blistering disorder, which affects the skin, eyes, and mucous membranes. The annual incidence of CP is 1/100,000. Esophageal involvement is rare and usually occurs in disseminated disease. Esophageal disease presents with dysphagia and weight loss and can be difficult to treat. We present a case of a 65-year-old woman with esophageal CP whose symptoms improved with esophageal dilatation and rituximab infusions.

Keywords: dysphagia; esophageal cicatricial pemphigoid; esophageal dilatation; rituximab.

Publication types

Case Reports