The oxidation of glycine and propionic acid in propionic acidemia with ketotic hyperglycinemia

Pediatr Res. 1972 Jun;6(6):576-83. doi: 10.1203/00006450-197206000-00006.
No abstract available

MeSH terms

  • Acidosis / blood
  • Acidosis / metabolism*
  • Body Fluids / analysis
  • Carbon Dioxide / biosynthesis
  • Carbon Isotopes
  • Child, Preschool
  • Female
  • Fibroblasts / enzymology
  • Glycine / blood
  • Glycine / metabolism*
  • Humans
  • Infant
  • Keto Acids / blood*
  • Ligases / metabolism
  • Male
  • Malonates / blood
  • Oxidation-Reduction
  • Propionates / blood
  • Propionates / metabolism*
  • Serine / biosynthesis

Substances

  • Carbon Isotopes
  • Keto Acids
  • Malonates
  • Propionates
  • Carbon Dioxide
  • Serine
  • Ligases
  • Glycine